MANAGEMENT OF CERVICOFACIAL CYSTIC LYMPHANGIOMA IN CHILDREN

Dr Mouangue-Mbonjo  Louise; Dr Diallo Mamadou Mouctar Ramata; Dr Minka Ngom Esthelle Geneviève Stéphanie; Dr Badang Ambadiang Florent Dimitri; Pr Njifou Njimah Amadou

doi:10.5281/zenodo.13892285

Authors

Dr Mouangue-Mbonjo Louise Lecturer / ENT and Maxillofacial Surgery Department
Dr Diallo Mamadou Mouctar Ramata Department of Otorhinolaryngology and Cervico-maxillofacial Surgery
Dr Minka Ngom Esthelle Geneviève Stéphanie Lecturer / Otorhinolaryngology Unit of the Douala General Hospital
Dr Badang Ambadiang Florent Dimitri Department and CervicoMaxillo-Facial Surgery
Pr Njifou Njimah Amadou Faculty of Medicine and Pharmaceutical Sciences

DOI:

https://doi.org/10.5281/zenodo.13892285

Keywords:

Cervicofacial, cystic, lymphangioma, diagnosis, treatment, surgery

Abstract

Introduction: Cystic lymphangioma is a rare, benign, tumor of the lymphatic vessels. It has varying locations, with the commonest being the cervicofacial region. This study aimed to describe the clinical characteristics and outcomes of patients with cervicofacial cystic lymphangioma. Materials and Methods: This was a retrospective study of 24 patients who underwent surgery for head and neck lymphangioma between 2013 and 2023 in XX hospital. The studied variables included age, sex, symptoms, imaging findings, results, and complications. Results: Most of the patients were male (58.3%). The median patient age was 4.5 (2.0–6.7) years. Fifty percent (n=12) of patients had visible lesions at birth, and 16 (66.7%) had left-sided lesions. The shoulder (n=3; 12.5%), clavicle (n=2; 8.3%), and mandible (n=2; 8.3%) were the main sites of extension. Imaging examination was performed in nine (37.5%). Eighteen (87.5%) patients underwent total excision of the tumor. Furthermore, six (25.0%) patients had received preoperative sclerotherapy. Postoperative complications were observed in 25.0% of the patients, with lymphedema (n=6) being the commonest. Esthetic sequelae were the commonest sequelae in 37.5% (n=9) of patients. No death was registered. Conclusion: Cystic cervicofacial lymphangioma is a complex pathology requiring multidisciplinary management. Sclerotherapy leads to good outcomes in compressive forms.

Author Biographies

Dr Mouangue-Mbonjo Louise, Lecturer / ENT and Maxillofacial Surgery Department

Lecturer / ENT and Maxillofacial Surgery Department, Yaounde Central Hospital, Department of Otorhinolaryngology and Cervico-maxillofacial Surgery, Yaounde Central Hospital, Faculty of Medicine and Pharmaceutical Sciences, University of Douala, Cameroon

Dr Diallo Mamadou Mouctar Ramata, Department of Otorhinolaryngology and Cervico-maxillofacial Surgery

Medical Practician / Regional Hospital of Mamou, Department of Otorhinolaryngology and Cervico-maxillofacial Surgery, Mamou, Guinea

Dr Minka Ngom Esthelle Geneviève Stéphanie, Lecturer / Otorhinolaryngology Unit of the Douala General Hospital

Lecturer / Otorhinolaryngology Unit of the Douala General Hospital, Faculty of Medicine and Pharmaceutical Sciences, University of Douala, Cameroon

Dr Badang Ambadiang Florent Dimitri, Department and CervicoMaxillo-Facial Surgery

Lecturer, ENT Department and CervicoMaxillo-Facial Surgery, Regional Military Hospital No. 2 Douala, Faculty of Medicine and Pharmaceutical Sciences of the University of Douala, Cameroon

Pr Njifou Njimah Amadou, Faculty of Medicine and Pharmaceutical Sciences

Senior lecturer / Faculty of Medicine and Pharmaceutical Sciences, University of Douala, Cameroon

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